Delayed cochlear implantation in post-meningitic deafness and hereditary complement C2 deficiency

Research output: Contribution to journalArticle

Standard

Delayed cochlear implantation in post-meningitic deafness and hereditary complement C2 deficiency. / Di Berardino, Federica; Truedsson, Lennart; Zanetti, Diego.

In: International Journal of Pediatric Otorhinolaryngology Extra, Vol. 15, 01.01.2017, p. 4-8.

Research output: Contribution to journalArticle

Harvard

APA

CBE

MLA

Vancouver

Author

RIS

TY - JOUR

T1 - Delayed cochlear implantation in post-meningitic deafness and hereditary complement C2 deficiency

AU - Di Berardino, Federica

AU - Truedsson, Lennart

AU - Zanetti, Diego

PY - 2017/1/1

Y1 - 2017/1/1

N2 - We report the case of an adolescent with post-verbal severe/profound sensorineural hearing loss, occurring as a consequence of two bouts of pneumococcal meningitis at 12 and 32 months of age. A possible immunodeficiency was investigated, revealing hereditary complement C2 deficiency (C2D). Given the insufficient benefit from high-power hearing aids, the boy received a cochlear implant (CI) at age 12. Despite the long interval of partial hearing deprivation and the post-meningitic etiology, improvement in open-set speech perception and quality of life were observed. The C2D did not favour post-operative infections nor meningitis recurrence. The risks and benefit of CI in this peculiar clinical circumstance are discussed after reviewing the literature.

AB - We report the case of an adolescent with post-verbal severe/profound sensorineural hearing loss, occurring as a consequence of two bouts of pneumococcal meningitis at 12 and 32 months of age. A possible immunodeficiency was investigated, revealing hereditary complement C2 deficiency (C2D). Given the insufficient benefit from high-power hearing aids, the boy received a cochlear implant (CI) at age 12. Despite the long interval of partial hearing deprivation and the post-meningitic etiology, improvement in open-set speech perception and quality of life were observed. The C2D did not favour post-operative infections nor meningitis recurrence. The risks and benefit of CI in this peculiar clinical circumstance are discussed after reviewing the literature.

KW - Adolescence

KW - C2

KW - Cochlear implantation

KW - Complement deficiency

KW - Immunological

KW - Meningitis

UR - http://www.scopus.com/inward/record.url?scp=85007553549&partnerID=8YFLogxK

U2 - 10.1016/j.pedex.2016.11.002

DO - 10.1016/j.pedex.2016.11.002

M3 - Article

VL - 15

SP - 4

EP - 8

JO - International Journal of Pediatric Otorhinolaryngology Extra

T2 - International Journal of Pediatric Otorhinolaryngology Extra

JF - International Journal of Pediatric Otorhinolaryngology Extra

SN - 1871-4048

ER -