Sammanfattning
We report a case of congenital absence of the portal vein (CAPV) in an adult male who underwent resection for hepatocellular carcinoma. CAPV is a rare anomaly; only 29 cases, mostly in children, have been presented to date. An association between CAPV and cardiac abnormalities, polysplenia syndrome, skeletal abnormalities and liver tumors has been seen in children. To the best of our knowledge this is the first case of CAPV in an adult male resected for hepatocellular carcinoma. However, since CAPV can be without symptoms, the number of undiagnosed cases is not known.
Originalspråk | engelska |
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Sidor (från-till) | 2228-2231 |
Antal sidor | 4 |
Tidskrift | European Radiology |
Volym | 11 |
Nummer | 11 |
DOI | |
Status | Published - 2001 jan. 1 |
Externt publicerad | Ja |
Ämnesklassifikation (UKÄ)
- Pediatrik